Papillophlebitis is believed to be an inflammatory variant of CRVO in young patients. Typical appearance consists of scattered retinal hemorrhages most prominent in the periphery and a swollen optic nerve. Optic nerve swelling is out of proportion with the retinal hemes. Veins are dilated. IVFA appearance is identical to a non-ischemic CRVO.

During the initial attack, patients may complain of a visual aura similar to a migraine episode. Visual acuity is usually only mildly reduced and a full recovery within 12-18 months is the norm. Blind spot enlargement is the most common visual field defect.

A link to mitral valve prolapse has been reported.

There is no treatment. Is this reallly a separate entity?

Papillophlebitis
Non-ischemic CRVO